- Case Report
- Hemophagocytic Syndrome with Kawasaki
Disease and Peripheral Gangrene
-
Hwa Jun Yun, Ko Woon Jeon, Hwang Min Kim, Seok Won Park, Young Uh
-
Clin Exp Pediatr. 2002;45(5):664-668. Published online May 15, 2002
-
|
A twenty six months-old boy developed hemophagocytic syndrome during the course of Kawasaki disease. Despite the appropriate treatment modalities for Kawasaki disease, he developed thrombocytopenia, hepatomegaly, high-grade fever, hypertriglyceridemia, peripheral gangrene, and evidence of hemophagocytosis in bone marrow biopsy. Although the course was stormy, he responded well to a combination therapy of corticosteroid and etoposide. |
-
-
- Original Article
- Non-Hemolytic Hereditary Ellitocytosis born of Asymptomatic Carrier state of Hereditary Elliticytosis.
-
Hae Joon Park, In Soon Ahn, Baek Keun Lim, Young Uh, Kyung Won Lee
-
Clin Exp Pediatr. 1988;31(1):113-118. Published online January 31, 1988
-
|
Hereditary elliptocytosis is characterized by elliptically shaped erythrocytes in peripheral blood
and known to be transmitted as an autosomal dominant trait, but in some cases, inherited recessively.
The clinical and hematologic expressions are variable range from healthy person with normal red cell
morphology to severe hemolytic anemia.
Recently, the authors experienced all three offsprings shown non-hemolytic hereditary el-
liptocytosis, whose parents were healthy persons with... |
-
-
|